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題名:當前重型海洋性貧血患童的治療與護理趨勢
書刊名:護理雜誌
作者:李雅玲林東燦
作者(外文):Lee, Y. L.Lin, D. T.
出版日期:1997
卷期:44:4
頁次:頁15-21
主題關鍵詞:重型海洋性貧血輸血排鐵療法排鐵劑治療護理Thalassemia majorBlood transfusionIron chelating agentDesferrioxamineDesferalTreatmentNursing care
原始連結:連回原系統網址new window
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  • 被引用次數被引用次數:期刊(1) 博士論文(0) 專書(0) 專書論文(0)
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  • 點閱點閱:39
     目前國內外對重型海洋性貧血(本文指p-重型海洋性貧血)患者的治療除了骨髓 移植有可能治癒外,患孩的一生必須仰賴輪血維生,且要面對輸血衍生的副作用,因而須 長時間的注射排鐵劑,以及症狀處理,例如脾臟切除等治療。醫吧遵從行為對重型海洋性 貧血患者的身體狀況控制及生活品質維持是非常必要且重要的關鍵。為使病患有良好的醫 囑遵從行為,應考慮病患個人因素、醫療情境因素、照顧者因素及病友、親友的支持等因 素。護埋這類病患的重點,建議是:(1)有計畫地提供資料,(2)進行身體評估,(3)提供熟 練的技術,(4)注意患孩心理、社會性需求,有耐心、技巧地輔導,(5)適度地參與病友組 織的活動。
期刊論文
1.Evans, L.、Spleman, M.(1983)。The problem of noncompliance with drug therapy。Drug,25(1),63-76。  new window
2.林國信(1993)。β-海洋性貧血。醫學繼續教育,3(6),727。  延伸查詢new window
3.林從慶、高志平(19890800)。小球性貧血之鑑別診斷及海洋型貧血之新近發展。臨床醫學,24(2)=140,129-134。new window  延伸查詢new window
4.林東燦(19931100)。β-海洋性貧血之傳統治療。醫學繼續教育,3(6),741-745。  延伸查詢new window
5.林凱信(19931100)。β-海洋性貧血的骨髓移植。醫學繼續教育,3(6),746-750。  延伸查詢new window
6.Cavill, I.、Ricketts, C.、Jacobs, A.、Letsky, E.(1978)。Erythropoiesis and the effect of transfusion in homozygous beta-thalassemia。New England Jounal of Medicine,298(14),776-778。  new window
7.Cazzla, M.、Borgna-Pignatti, C.、Locatelli, F.、Ponchio, L.、de Beguin, Y.、Stefano, P.(1997)。A moderate transfusion regimen may reduce iron loading in beta-thalassemia major without produing excessive expansion of erythropoiesis。Transfusion,37(2),135-140。  new window
8.Cheney, K.、Gumbiner, C.、Benson, B.、Tenenbein, M.(1995)。Survival after a severe iron poisoning treated with intermittent infusion of desferrioxamine。Journal of Toxicology-Clinical Toxicology,33(1),61-66。  new window
9.Hilbert, G. A.(1985)。Accuracy of selfreported measures of compliance。Nursing Research,34(5),319-320。  new window
10.Jones, T. W.、Boulware, S. D.(1993)。Correction of hyperinsulinemia by gly-buride treatment in nondiabetic patients with thalassemia major。Pediatric Research,33(5),497-500。  new window
11.Lombardo , T.、Ferro, G.、Frontini, V.、Percolla, S.(1996)。High-dose intravenous desferrioxamine (DFO) delivery in Lombardo, T. Four thalassemic patients allergic to subcutaneous DFO administration。American Journal of Haematology,51(1),90-92。  new window
12.Maj, M.、Magni, L. A.、Confalonier, C.(1995)。Evaluation of the compliance of thalassemic patients at a structured ambulatory day hospital。Pediatric Medicare Chirurgica,17(1),49-51。  new window
13.Oerter, K . E.、Kamp, G. A.、Munscon, P. J.、Nienhuis, A. W.、Cassorla, F. G.、Manasco, P. K.(1993)。Multiple hormone deficiencies in children with hemochromatosis。Journal of Clinical Endocrinology Metabolism,76(2),357-361。  new window
14.Propper, R. D.、Cooper, B.、Ruto, R. R.、Nienhuis, A. W.、Anderson, W.、Franklin, B.(1977)。Continuous subcutaneous administration of desferrioxamine in patients with iron overload。New England Journal of Medline,297(8),418-423。  new window
會議論文
1.Piomelli, S.(1978)。Desferrioxamine B chelation in the young thalassemia。Chelation Therapy in Chronic Iron Overload Symposium。Miami, Florida。  new window
 
 
 
 
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